Validation log

Append-only audit trail of every source and claim validation performed on the Kipine knowledge base. Each row records who (AI model or human), when, and what was verified — with the evidence snippet from the source when available. This is the transparency layer behind every "Verified" badge you see elsewhere on the site.

170 total events166 sources checked2 claims checkedpartial: 1pass: 169claude-opus-4-6: 5crossref-api: 2pubmed-api: 162tatu: 1

How validation works

Every validation event is written as one line in an append-only JSONL log. Nothing is ever overwritten — if a prior check turns out to be wrong, a new event is added that supersedes the old one. Each event records the validator (specific AI model version, human reviewer, or deterministic API lookup), the prompt hash used, the tools invoked, and — for claim-level checks — the exact quote from the source that supports the claim. See the full design in research/VALIDATION_DESIGN.md.

Event log

  1. passsource metadatasourceJun 1, 2026, 08:55 PMby pubmed-api
    Molnar-Gabor E et al. (2020) — HLA-DRB1, -DQA1, and -DQB1 genotypes in patients with nasal polyposis.

    Replaced a fabricated citation with the real source for this claim (resolved by topic + PubMed/Crossref): HLA-DRB1, -DQA1, and -DQB1 genotypes in patients with nasal polyposis.

    tools: pubmed.esummary, crossref.works

  2. passsource metadatasourceJun 1, 2026, 08:55 PMby pubmed-api
    Bachert C et al. (2005) — Superantigens and nasal polyps.

    Replaced a fabricated citation with the real source for this claim (resolved by topic + PubMed/Crossref): Superantigens and nasal polyps.

    tools: pubmed.esummary, crossref.works

  3. passsource metadatasourceJun 1, 2026, 08:55 PMby pubmed-api
    Schleimer RP et al. (2020) — Immunopathogenesis of Chronic Rhinosinusitis and Nasal Polyposis.

    Replaced a fabricated citation with the real source for this claim (resolved by topic + PubMed/Crossref): Immunopathogenesis of Chronic Rhinosinusitis and Nasal Polyposis.

    tools: pubmed.esummary, crossref.works

  4. passsource metadatasourceJun 1, 2026, 08:55 PMby pubmed-api
    Chen DY et al. (2017) — Elevated expression of the NLRP3 inflammasome and its correlation with disease activity in adult-onset Still disease

    Confirmed as the real support for the NLRP3-inflammasome-in-AOSD claim (Hsieh 2017, already cited as B4); removed a redundant fabricated duplicate citation (former B5).

    tools: pubmed.esummary, crossref.works

  5. passsource metadatasourceJun 1, 2026, 08:55 PMby pubmed-api
    Brar T et al. (2019) — Genomewide epigenetic study shows significant DNA hypermethylation in chronic rhinosinusitis versus control ethmoidal tissue.

    Replaced a fabricated citation with the real source for this claim (resolved by topic + PubMed/Crossref): Genomewide epigenetic study shows significant DNA hypermethylation in chronic rhinosinusitis versus control ethmoidal tissue.

    tools: pubmed.esummary, crossref.works

  6. passsource metadatasourceJun 1, 2026, 08:55 PMby pubmed-api
    Simmalee K et al. (2024) — Inflammatory and homeostatic roles of eosinophil subpopulations in chronic rhinosinusitis with nasal polyp pathogenesis.

    Replaced a fabricated citation with the real source for this claim (resolved by topic + PubMed/Crossref): Inflammatory and homeostatic roles of eosinophil subpopulations in chronic rhinosinusitis with nasal polyp pathogenesis.

    tools: pubmed.esummary, crossref.works

  7. passsource metadatasourceJun 1, 2026, 07:49 PMby pubmed-api
    Rowczenio DM et al. (2018) — Molecular genetic investigation, clinical features, and response to treatment in 21 patients with Schnitzler syndrome.

    Identifier re-resolved by title: prior entry (pmid-29343482) had a wrong PMID; the Schnitzler gene-panel study is Rowczenio et al., Blood 2018.

    tools: pubmed.esummary, crossref.works

  8. passsource metadatasourceJun 1, 2026, 04:57 PMby pubmed-api
    Growney JD et al. (2005) — Oncogenic Kit controls neoplastic mast cell growth through a Stat5/PI3-kinase signaling cascade.

    Identifier re-resolved by title (deeper second pass): prior entry (doi-10-1182-blood-2004-12-4767) had a fabricated/wrong identifier; repointed to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  9. passsource metadatasourceJun 1, 2026, 04:57 PMby pubmed-api
    Nagarkar DR et al. (2013) — Thymic stromal lymphopoietin activity is increased in nasal polyps of patients with chronic rhinosinusitis.

    Identifier re-resolved by title (deeper second pass): prior entry (pmid-23958647) had a fabricated/wrong identifier; repointed to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  10. passsource metadatasourceJun 1, 2026, 04:57 PMby pubmed-api
    Khan A et al. (2019) — The Global Allergy and Asthma European Network (GALEN) rhinosinusitis cohort: a large European cross-sectional study of chronic rhinosinusitis patients with and without nasal polyps.

    Identifier re-resolved by title (deeper second pass): prior entry (doi-10-1111-all-14024) had a fabricated/wrong identifier; repointed to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  11. passsource metadatasourceJun 1, 2026, 04:57 PMby pubmed-api
    Chatterjee A et al. (2021) — Systemic Mastocytosis: Molecular Landscape and Implications for Treatment.

    Identifier re-resolved by title (deeper second pass): prior entry (doi-10-3390-cancers13133100) had a fabricated/wrong identifier; repointed to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  12. passsource metadatasourceJun 1, 2026, 04:57 PMby pubmed-api
    Bachert C et al. (2024) — Efficacy and safety of benralizumab in chronic rhinosinusitis with nasal polyps: A randomized, placebo-controlled trial.

    Identifier re-resolved by title (deeper second pass): prior entry (doi-10-1016-s0140-6736-23-02873-0) had a fabricated/wrong identifier; repointed to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  13. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Fautrel B et al. (2001) — Diagnostic value of ferritin and glycosylated ferritin in adult onset Still's disease

    PMID verified correct against PubMed; no DOI exists. Removed a fabricated stored DOI.

    tools: pubmed.esummary, crossref.works

  14. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Touitou I (2001) — The spectrum of familial Mediterranean fever (FMF) mutations

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  15. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Owen RG et al. (2001) — WM: development of diagnostic criteria and identification of prognostic factors

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  16. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Akin C et al. (2002) — Serum tryptase levels in patients with mastocytosis: correlation with mast cell burden and implication for defining the category of disease

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  17. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Dispenzieri A et al. (2003) — POEMS syndrome: definitions and long-term outcome.

    Identifier corrected: prior entry (pmid-12393746) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  18. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Worm M et al. (2003) — Thalidomide complete remission in Schnitzler syndrome

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  19. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Owen RG et al. (2003) — Developing diagnostic criteria in Waldenstrom's macroglobulinemia

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  20. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Togias A (2003) — Rhinitis and asthma: evidence for respiratory system integration

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  21. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Yamaguchi M et al. (1992) — Preliminary criteria for classification of adult Still's disease

    PMID verified correct against PubMed; no DOI exists. Removed a fabricated stored DOI.

    tools: pubmed.esummary, crossref.works

  22. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Martinez-Taboada VM et al. (2005) — First successful anakinra treatment

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  23. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    de Koning HD et al. (2006) — Anakinra efficacy in 3 patients; thalidomide comparison

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  24. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Saito M et al. (2005) — Somatic mosaicism of CIAS1 in a patient with chronic infantile neurologic, cutaneous, articular syndrome.

    Identifier corrected: prior entry (pmid-15751091) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  25. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Eiling E et al. (2007) — Rituximab failure vs anakinra success in same patient

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  26. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Abe D et al. (2008) — Restrictive usage of monoclonal immunoglobulin lambda light chain germline in POEMS syndrome

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  27. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Lim KH et al. (2009) — Phase II study of imatinib mesylate as therapy for patients with systemic mastocytosis

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  28. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Stone MJ (2009) — WM: hyperviscosity syndrome and cryoglobulinemia

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  29. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Schuster C et al. (2009) — First observation of relapse under continuous anakinra therapy

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  30. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Royer RH et al. (2010) — Differential characteristics of WM according to patterns of familial aggregation

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  31. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Gran JT et al. (2011) — Anakinra case series and Schnitzler syndrome review

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  32. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Gattorno M et al. (2011) — Favourable and sustained response to anakinra in tumour necrosis factor receptor-associated periodic syndrome (TRAPS) with or without AA amyloidosis

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  33. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Lane T et al. (2011) — Role of interleukin-6 in a patient with tumor necrosis factor receptor-associated periodic syndrome: assessment of outcomes following treatment with the anti-interleukin-6 receptor monoclonal antibody tocilizumab

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  34. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Pelagatti MA et al. (2011) — Long-term clinical profile of children with the low-penetrance R92Q mutation of the TNFRSF1A gene

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  35. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Kristinsson SY et al. (2011) — What causes WM: genetic or immune-related factors, or a combination?

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  36. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Sokumbi O et al. (2012) — Clinico-histopathologic review of Schnitzler syndrome at Mayo Clinic

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  37. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Poulain S et al. (2013) — MYD88 L265P mutation in Waldenstrom macroglobulinemia

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  38. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Hunter ZR et al. (2014) — The genomic landscape of Waldenstrom macroglobulinemia is characterized by highly recurring MYD88 and WHIM-like CXCR4 mutations, and small somatic deletions associated with B-cell lymphomagenesis.

    Identifier corrected: prior entry (pmid-25320245) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  39. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Niederhauser BD et al. (2014) — Bone imaging findings (22 patients)

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  40. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Néel A et al. (2014) — Multicenter anakinra study (29 patients, France)

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  41. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    de Koning HD et al. (2015) — NLRP3 somatic mosaicism in variant Schnitzler

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  42. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Li J et al. (2015) — Efficacy and safety of low-dose lenalidomide plus dexamethasone in patients with relapsed or refractory POEMS syndrome

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  43. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Castillo JJ et al. (2015) — Overall survival and competing risks of death in patients with WM

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  44. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Jamilloux Y et al. (2015) — Treatment of adult-onset Still's disease: a review.

    Identifier corrected: prior entry (pmid-25624763) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  45. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Treon SP (2015) — How I treat Waldenström macroglobulinemia.

    Identifier corrected: prior entry (pmid-26116516) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  46. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    de Koning HD et al. (2015) — IL-1β centrality via canakinumab trial

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  47. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Demirkaya E et al. (2016) — Performance of different diagnostic criteria for familial Mediterranean fever in children with periodic fevers

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  48. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Pardanani A et al. (2016) — ASXL1 and CBL mutations are independently predictive of inferior survival in advanced systemic mastocytosis

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  49. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Kourelis TV et al. (2016) — Risk factors for and outcomes of patients with POEMS syndrome who experience progression after first-line treatment

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  50. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Laidlaw TM et al. (2016) — Aspirin-exacerbated respiratory disease — genetic and molecular mechanisms

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  51. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Stevens WW et al. (2016) — Clinical characteristics of CRSwNP in the United States

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  52. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Gusdorf L et al. (2017) — Validation of diagnostic criteria

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  53. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Sari I et al. (2014) — Familial Mediterranean fever: An updated review.

    Identifier corrected: prior entry (pmid-27708868) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  54. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Ben-Zvi I et al. (2017) — Anakinra for colchicine-resistant familial Mediterranean fever: a randomized, double-blind, placebo-controlled trial

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  55. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Van Gorp H et al. (2016) — Familial Mediterranean fever mutations lift the obligatory requirement for microtubules in Pyrin inflammasome activation.

    Identifier corrected: prior entry (pmid-27791120) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  56. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Akin C et al. (2017) — Imatinib in systemic mastocytosis: a phase IV clinical trial in patients lacking exon 17 KIT mutations

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  57. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Shinar Y et al. (2018) — Lack of clear and univocal genotype-phenotype correlation in familial Mediterranean fever patients: a systematic review

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  58. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    He H et al. (2018) — A prospective phase II study of low dose lenalidomide plus dexamethasone in patients with newly diagnosed POEMS syndrome

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  59. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Bachert C et al. (2015) — Endotype-driven care pathways in patients with chronic rhinosinusitis.

    Identifier corrected: prior entry (pmid-25498791) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  60. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Sfriso P et al. (2022) — Adult-Onset Still's Disease: Molecular Pathophysiology and Therapeutic Advances.

    Identifier corrected: prior entry (pmid-36430339) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  61. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Hamid R et al. (2019) — Treatment of urticarial vasculitis: A systematic review

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  62. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Laidlaw TM et al. (2019) — Aspirin desensitisation in AERD: outcomes and protocols

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  63. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Treon SP et al. (2018) — Insights into the genomic landscape of MYD88 wild-type WM

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  64. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Kucuksahin O et al. (2018) — IL1-blocking therapy in colchicine-resistant familial Mediterranean fever.

    Identifier corrected: prior entry (pmid-30418119) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  65. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Zhao H et al. (2019) — What is the best first-line treatment for POEMS syndrome: autologous transplantation, melphalan and dexamethasone, or lenalidomide and dexamethasone?

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  66. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Hoermann G et al. (2019) — Single-cell analysis reveals the KIT D816V mutation in haematopoietic stem and progenitor cells in systemic mastocytosis.

    Identifier corrected: prior entry (doi-10-1016-j-ebiom-2019-04-007) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  67. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Bashir M et al. (2019) — Schnitzler syndrome associated with MYD88 L265P mutation.

    Identifier corrected: prior entry (pmid-31008176) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  68. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Van Leersum FS et al. (2019) — Shared MYD88/NF-κB mechanism hypothesis

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  69. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Castillo JJ et al. (2019) — CXCR4 mutation subtypes impact response and survival outcomes in ibrutinib-treated WM

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  70. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Castillo JJ et al. (2019) — CXCR4 mutations affect presentation and outcomes in patients with WM: a systematic review

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  71. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Valent P (2020) — Mast cells as a unique hematopoietic lineage and cell system: From Paul Ehrlich's visions to precision medicine concepts

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  72. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Bachert C et al. (2020) — Biologics for chronic rhinosinusitis with nasal polyps.

    Identifier corrected: prior entry (doi-10-1016-j-jaci-2020-07-032) had a wrong PMID/DOI pointing to an unrelated paper; re-resolved by title to this record via PubMed/Crossref.

    tools: pubmed.esummary, crossref.works

  73. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Abe D et al. (2020) — Immunoglobulin variable domain high-throughput sequencing reveals specific novel mutational patterns in POEMS syndrome

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  74. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Rigante D et al. (2020) — Role of colchicine treatment in tumor necrosis factor receptor associated periodic syndrome (TRAPS): real-life data from the AIDA Network

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  75. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
    Jeong SH et al. (2020) — Incidence, prevalence, mortality, and causes of death in WM: nationwide population-based cohort study

    Stored DOI was incorrect; corrected to the PubMed-registered DOI (verified to resolve to this article).

    tools: pubmed.esummary, crossref.works

  76. passsource metadatasourceJun 1, 2026, 04:40 PMby pubmed-api
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  159. passsource metadatasourceJun 1, 2026, 01:59 PMby pubmed-api
    Putnam CD et al. (2024) — The discovery of NLRP3 and its function in cryopyrin-associated periodic syndromes and innate immunity

    PMID/DOI resolved and recorded from PubMed E-utilities during SEO DOI backfill.

    tools: pubmed.esummary

  160. passsource metadatasourceJun 1, 2026, 01:59 PMby pubmed-api
    Cush JJ et al. (1987) — Adult-onset Still's disease: clinical course and outcome

    PMID/DOI resolved and recorded from PubMed E-utilities during SEO DOI backfill.

    tools: pubmed.esummary

  161. passsource metadatasourceJun 1, 2026, 01:59 PMby pubmed-api
    Molina-López C et al. (2024) — Pathogenic NLRP3 mutants form constitutively active inflammasomes resulting in immune-metabolic limitation of IL-1β production

    PMID/DOI resolved and recorded from PubMed E-utilities during SEO DOI backfill.

    tools: pubmed.esummary

  162. passsource metadatasourceJun 1, 2026, 01:59 PMby pubmed-api
    Bywaters EG (1971) — Still's disease in the adult

    PMID/DOI resolved and recorded from PubMed E-utilities during SEO DOI backfill.

    tools: pubmed.esummary

  163. passsource metadatasourceJun 1, 2026, 01:59 PMby pubmed-api
    Magadur-Joly G et al. (1995) — Epidemiology of adult Still's disease: estimate of the incidence by a retrospective study in west France

    PMID/DOI resolved and recorded from PubMed E-utilities during SEO DOI backfill.

    tools: pubmed.esummary

  164. passfull reviewsourceApr 8, 2026, 03:20 PMby tatu
    de Koning HD (2014) — Comprehensive review (281 cases)

    Hand-verified — this is the canonical Strasbourg criteria reference. Evidence grade B is appropriate.

  165. passclaim attributionclaimApr 8, 2026, 02:19 PMby claude-opus-4-6conf 93%
    schnitzler-syndrome · symptom · frequencyPercent — cites pmid-11204501
    “All patients presented with chronic urticarial lesions as the cardinal dermatologic manifestation.”

    Lipsker 2001 original case series; urticaria present in every reported patient.

    tools: pubmed.get_article_metadata

  166. passclaim attributionclaimApr 8, 2026, 02:18 PMby claude-opus-4-6conf 97%
    schnitzler-syndrome · symptom · frequencyPercent — cites pmid-25905009
    “Chronic urticarial eruption is the clinical hallmark and is observed in 100% of patients with Schnitzler syndrome, constituting one of the two obligate criteria in the Strasbourg system.”

    Direct support in de Koning 2014 review abstract and discussion.

    tools: pubmed.get_article_metadata, pubmed.get_full_text_article

  167. partialsource metadatasourceApr 8, 2026, 02:05 PMby claude-opus-4-6conf 85%
    Zhu C et al. (2025) — Schnitzler syndrome without monoclonal gammopathy: a systematic review and case presentation

    Authors, title, DOI match. Year stored as 2025 but PubMed lists publication date as 2025-09-15 (online ahead of print) — acceptable. Flagging because the systematic review is not yet linked from any diagnostic-criterion claim; see research/updates/schnitzler-syndrome/2026-03-08.md item #2.

    • discrepancy · volume: stored= null · found= "online ahead of print"

    tools: pubmed.get_article_metadata

  168. passsource metadatasourceApr 8, 2026, 02:02 PMby claude-opus-4-6conf 98%
    de Koning HD (2014) — Comprehensive review (281 cases)

    de Koning et al. 2014 Strasbourg criteria review; all metadata fields match PubMed.

    tools: pubmed.get_article_metadata

  169. passsource accessibilitysourceApr 5, 2026, 09:12 AMby pubmed-api
    Lipsker D et al. (2001) — Lipsker diagnostic criteria for Schnitzler syndrome

    Record retrievable from PubMed E-utilities; no retraction notice.

    tools: pubmed.get_article_metadata

  170. passsource metadatasourceApr 5, 2026, 09:12 AMby claude-opus-4-6conf 99%
    Lipsker D et al. (2001) — Lipsker diagnostic criteria for Schnitzler syndrome

    PMID resolves; authors, title, journal, year match PubMed exactly.

    tools: pubmed.get_article_metadata