significantNew research
French national series quantifies AA amyloidosis severity in TRAPS
TNF Receptor-Associated Periodic Syndrome →Summary
Delaleu et al. (2021) reported that AA amyloidosis preceded TRAPS diagnosis in 96% of cases, with 47% needing renal replacement therapy and 14% mortality. Highlights the importance of early TRAPS diagnosis.
Source
Grade Bcase series and review
Tumour necrosis factor receptor-1 associated periodic syndrome (TRAPS)-related AA amyloidosis: a national case series and systematic review
Delaleu J, Deshayes S, Rodrigues F, Savey L, Rivière E, Martin Silva N, Aouba A, Amselem S, Rabant M, Grateau G, Giurgea I, Georgin-Lavialle S · Rheumatology (Oxford) · 2021
- •AA amyloidosis preceded TRAPS diagnosis in 96% of cases
- •47% required renal replacement therapy
- •14% mortality after median 23-month follow-up
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ID: traps-update-2Type: new_researchImpact: significant