Tumour necrosis factor receptor-1 associated periodic syndrome (TRAPS)-related AA amyloidosis: a national case series and systematic review

Delaleu J, Deshayes S, Rodrigues F, Savey L, Rivière E, Martin Silva N, Aouba A, Amselem S, Rabant M, Grateau G, Giurgea I, Georgin-Lavialle S

Rheumatology (Oxford) · 2021

Grade Bcase series and review
DOI ↗PubMed ↗

Key Findings

  • ●AA amyloidosis preceded TRAPS diagnosis in 96% of cases
  • ●47% required renal replacement therapy
  • ●14% mortality after median 23-month follow-up
  • ●Biologic treatment preserved residual renal function

Referenced in (1 disease)

TNF Receptor-Associated Periodic Syndrome
ID: pmid-33715002DOI: 10.1093/rheumatology/keab252PMID: 33715002