significantMechanism
Anti-C1q antibodies shown to directly activate classical complement pathway in HUVS
Hypocomplementemic Urticarial Vasculitis Syndrome →Summary
Bhatt et al. demonstrated that anti-C1q antibodies in HUVS bind to the collagen-like region of C1q, preventing C1q from clearing immune complexes while simultaneously activating the classical complement pathway at the endothelial surface. This dual mechanism explains the paradox of hypocomplementemia with ongoing complement-mediated tissue damage.
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ID: hypocomplementemic-urticarial-vasculitis-syndrome-update-6Type: mechanismImpact: significant