incrementalepidemiology
Systematic review estimates HUVS prevalence at fewer than 1 per million
Hypocomplementemic Urticarial Vasculitis Syndrome →Summary
A systematic literature review identified fewer than 250 published HUVS cases worldwide, estimating prevalence below 1 per million. The review confirmed female predominance (3:1 ratio), mean age of onset in the 4th decade, and SLE overlap in approximately 50% of cases, underscoring the need for international registries.
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ID: hypocomplementemic-urticarial-vasculitis-syndrome-update-9Type: epidemiologyImpact: incremental