significantclassification change
HUVS reclassified as 'anti-C1q vasculitis' in Chapel Hill nomenclature
Hypocomplementemic Urticarial Vasculitis Syndrome →Summary
The 2012 revised International Chapel Hill Consensus Conference classified HUV as 'anti-C1q vasculitis', formally recognizing it as a distinct small vessel vasculitis entity associated with anti-C1q antibodies, urticaria, and hypocomplementemia.
Source
Grade Aexpert opinion
2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides
Jennette JC, Falk RJ, Bacon PA, Basu N, Cid MC, et al. · Arthritis Rheum · 2013
- •Classified HUV as 'anti-C1q vasculitis' in the revised nomenclature
- •Defined as vasculitis with urticaria and hypocomplementemia affecting small vessels
- •Associated with anti-C1q antibodies, glomerulonephritis, obstructive pulmonary disease
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ID: hypocomplementemic-urticarial-vasculitis-syndrome-update-1Type: classification_changeImpact: significant