Monoclonal gammopathies of cutaneous significance: A nomenclature and pathophysiology-based classification.

Mir TH, Patell R, Freed JA

J Am Acad Dermatol · 2026

Grade Dletter

Key Findings

  • Proposes nomenclature framework for monoclonal gammopathies of cutaneous significance (MGCS)
  • Classifies Schnitzler syndrome within pathophysiology-based MGCS taxonomy
  • Distinguishes Schnitzler syndrome from other MGCS including POEMS, TEMPI, and scleromyxedema
  • Supports standardised language to improve recognition and reporting of Schnitzler syndrome

Referenced in (1 disease)

ID: pmid-41740896DOI: 10.1016/j.jaad.2025.12.126PMID: 41740896