[What is an undifferentiated systemic autoinflammatory disease in adults? Current state of knowledge and practical approach].

Mertz P, Chauffier J, Delplanque M

Rev Med Interne · 2025

Grade Creview

Key Findings

  • French-language review of undifferentiated systemic autoinflammatory diseases (SAIDs) in adults
  • Discusses innate immunity dysregulation and differential diagnosis including Schnitzler syndrome
  • Provides practical diagnostic approach to distinguishing undifferentiated SAID from defined entities
  • Relevant to Schnitzler syndrome evaluation in patients without classic gammopathy

Referenced in (1 disease)

ID: pmid-41271522DOI: 10.1016/j.revmed.2025.11.003PMID: 41271522