[What is an undifferentiated systemic autoinflammatory disease in adults? Current state of knowledge and practical approach].
Mertz P, Chauffier J, Delplanque M
Rev Med Interne · 2025
Grade Creview
Key Findings
- ●French-language review of undifferentiated systemic autoinflammatory diseases (SAIDs) in adults
- ●Discusses innate immunity dysregulation and differential diagnosis including Schnitzler syndrome
- ●Provides practical diagnostic approach to distinguishing undifferentiated SAID from defined entities
- ●Relevant to Schnitzler syndrome evaluation in patients without classic gammopathy
Referenced in (1 disease)
ID: pmid-41271522DOI: 10.1016/j.revmed.2025.11.003PMID: 41271522