Treatment and long-term follow-up of pediatric patients with hypocomplementemic urticarial vasculitis syndrome (HUVS): a case-based review

Key Findings

• ●Long-term follow-up of two DNASE1L3-mutant siblings over 20 years
• ●Rituximab most effective long-term treatment
• ●Renal involvement in 82% of pediatric HUVS patients
• ●Lupus nephritis most common renal manifestation

Referenced in (1 disease)