Acquired autoinflammatory disorders: a dermatologist's perspective.

Key Findings

• ●Comprehensive dermatology review of acquired autoinflammatory disorders including Schnitzler syndrome, AOSD, VEXAS, Kikuchi-Fujimoto disease, and HLH
• ●Schnitzler syndrome presented as a paradigm of acquired autoinflammatory disease with multifactorial pathogenesis
• ●Distinguishes autoinflammatory disorders from connective tissue diseases by negative ANA
• ●Highlights expanding genetic spectrum of acquired autoinflammatory disorders since VEXAS description
• ●Cutaneous manifestations are often the earliest diagnostic clue; detailed histopathologic classification provided

Referenced in (1 disease)