Systemic mastocytosis in adults: 2023 update on diagnosis, risk stratification and management

Pardanani A

Am J Hematol · 2023

Grade Anarrative review

Key Findings

  • Updated WHO 2022 and ICC criteria for SM diagnosis
  • KIT D816V VAF >=10% now a B-finding
  • CD30 added as minor criterion
  • Avapritinib approved for ISM

Referenced in (1 disease)

ID: pmid-37309222DOI: 10.1002/ajh.26962PMID: 37309222