POEMS Syndrome: 2019 Update on diagnosis, risk-stratification, and management

Dispenzieri A

Am J Hematol · 2019

Grade Anarrative review

Key Findings

  • Updated Dispenzieri diagnostic criteria with mandatory, major, and minor criteria
  • VEGF elevated as major criterion alongside sclerotic bone lesions and Castleman disease
  • 10-year OS approaching 80% in modern era

Referenced in (1 disease)

ID: pmid-31012139DOI: 10.1002/ajh.25495PMID: 31012139