Clues to detect tumor necrosis factor receptor-associated periodic syndrome (TRAPS) among patients with idiopathic recurrent acute pericarditis: results of a multicentre study
Cantarini L, Lucherini OM, Brucato A, Barone L, Cumetti D, Iacoponi F, Rigante D, et al.
Clin Res Cardiol · 2012
Grade Bcohortn=131
Key Findings
- ●6.1% of recurrent pericarditis patients carried TNFRSF1A mutations
- ●TRAPS patients with pericarditis had more recurrences and needed immunosuppression
- ●Poor colchicine response is a clue to TRAPS-associated pericarditis
Referenced in (1 disease)
ID: pmid-22311714DOI: 10.1007/s00392-012-0422-8PMID: 22311714