MYD88

Genetic findings for MYD88 in POEMS Syndrome

Variants (1)

VariantTypeFrequencySignificance
Somatic mutations (including L265P)somaticRare (identified in Chen et al. 2021 WES)MYD88 mutations detected in some POEMS patients, though at lower frequency than in Waldenstrom macroglobulinemia (>90%). Drives NF-kB activation. Overlap with Waldenstrom and Schnitzler syndrome pathogenesis.

Clinical implications

Somatic mutations (including L265P)

May predict response to ibrutinib or other BTK inhibitors.

Also found in: Waldenstrom macroglobulinemia (>90%), Schnitzler syndrome (~30%)