CUX1

Genetic findings for CUX1 in POEMS Syndrome

Variants (1)

VariantTypeFrequencySignificance
Recurrently mutated (somatic)somatic19% (Chen et al. 2021)Most frequently mutated gene in the Chen et al. (2021) targeted sequencing cohort. CUX1 is a transcription factor involved in cell cycle regulation. Loss-of-function mutations may contribute to clonal expansion.

Clinical implications

Recurrently mutated (somatic)

Research finding — no current clinical application.

Also found in: Myeloid neoplasms (Variable)