IL-1β

Central pathogenic driver

Expression
Elevated
Evidence level
established
Targeted by
Anakinra, Canakinumab

Role in pathogenesis

IL-1β is the key cytokine driving Schnitzler inflammation. Proven by the dramatic, rapid response to anakinra — symptoms resolve within hours, confirming IL-1β as the effector molecule.

Targeting drugs (2)

DrugMechanismResponseLine
AnakinraIL-1 receptor antagonist~94%1st
CanakinumabAnti–IL-1β monoclonal antibodyHigh (RCT confirmed)2nd

Sources (4)

Detailsde Koning HD et al. (2015) IL-1β centrality via canakinumab trial · Arthritis Res TherDOI
DetailsMartinez-Taboada VM et al. (2005) First successful anakinra treatment · Arthritis RheumDOI
DetailsNéel A et al. (2014) Multicenter anakinra study (29 patients, France) · Autoimmun RevDOI
DetailsLipsker D (2010) Schnitzler syndrome as paradigm of acquired autoinflammatory disease · Orphanet J Rare DisDOI