IL18

Genetic findings for IL18 in Adult-Onset Still's Disease

Variants (1)

VariantTypeFrequencySignificance
Promoter polymorphisms (S01/S01 diplotype); -607 promoter polymorphismgermlineS01/S01 diplotype significantly enriched in AOSD patients; seven SNPs and one 9bp insertion identifiedIL-18 gene promoter polymorphisms represent a major genetic risk factor for AOSD susceptibility, correlating with the characteristically elevated IL-18 serum levels

Clinical implications

Promoter polymorphisms (S01/S01 diplotype); -607 promoter polymorphism

The -607 promoter polymorphism has functional associations with disease course; certain genotypes may be protective against severity and chronic arthritis

Also found in: Systemic JIA (Similar associations reported)

Related hypotheses

Genetic susceptibility via HLA polymorphisms and autoinflammatory gene variants predisposes to AOSD

45
emerging·12 studies

Sources (1)

DetailsSugiura T et al. (2002) Association between adult-onset Still's disease and interleukin-18 gene polymorphisms · Genes ImmunDOI